Case of congenital Langerhans cells histiocytosis in an infant
https://doi.org/10.17650/1818-8346-2011-6-2-19-22
Abstract
In this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characterized. Authors concluded that timely diagnostics is very important to risk-adapted therapy at children with LCH.
About the Authors
T. T. Valiev
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
L. A. Makhonova
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
A. M. Kovrigina
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
E. N. Sholokhova
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
N. N. Tupitsyn
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
I. N. Serebryakova
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
G. L. Mentkevich
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Russian Federation
Russian Federation
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Review
For citations:
Valiev T.T., Makhonova L.A., Kovrigina A.M., Sholokhova E.N., Tupitsyn N.N., Serebryakova I.N., Mentkevich G.L. Case of congenital Langerhans cells histiocytosis in an infant. Oncohematology. 2011;6(2):19-22. (In Russ.) https://doi.org/10.17650/1818-8346-2011-6-2-19-22
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