Рекомендации Российского Совета экспертов по диагностике и лечению больных первичной иммунной тромбоцитопенией
Аннотация
Представлены новые рекомендации по диагностике и лечению первичной иммунной тромбоцитопении (ИТП) у взрослых и детей, разработанные на основе современных знаний о патогенезе заболевания и учитывающие возможности гематологической практики в России. Рекомендации основаны на согласованном мнении ведущих международных и российских экспертов по ИТП. Отмечены особенности диагностики ИТП и предложены различные варианты лечения 1, 2 и 3-й линий, включающие новые эффективные лекарственные препараты, недавно появившиеся на российском рынке, в частности, агонисты тромбопоэтиновых рецепторов (ромиплостим, элтромбопаг), значительно расширившие возможности консервативного лечения заболевания. Представленные рекомендации могут помочь специалистам-гематологам выработать индивидуальную тактику ведения каждого конкретного больного ИТП и улучшить качество жизни пациентов.
Ключевые слова
Об авторах
А. А. МасчанРоссия
Алексей Александрович Масчан
ФГУ Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии
Москва
А. Г. Румянцев
Россия
ФГУ Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии
Москва
Л. Г. Ковалева
Россия
Гематологический научный центр
Москва
Б. В. Афанасьев
Россия
Институт детской гематологии и трансплантологии
Санкт-Петербург
Т. И. Поспелова
Россия
кафедра терапии, гематологии и трансфузиологии
Новосибирск
А. Ю. Зарицкий
Россия
Санкт-Петербург
К. М. Абдулкадыров
Россия
Санкт-Петербург
В. В. Птушкин
Россия
ФГУ Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии
Москва
Н. В. Цветаева
Россия
Гематологический научный центр
Москва
И. А. Лисуков
Россия
Институт детской гематологии и трансплантологии
Санкт-Петербург
Г. Н. Салогуб
Россия
Санкт-Петербург
А. К. Голенков
Россия
Москва
Н. В. Медведева
Россия
Санкт-Петербург
О. А. Рукавицын
Россия
Москва
В. Л. Иванова
Россия
Москва
И. В. Маркова
Россия
Институт детской гематологии и трансплантологии
Санкт-Петербург
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Рецензия
Для цитирования:
Масчан А.А., Румянцев А.Г., Ковалева Л.Г., Афанасьев Б.В., Поспелова Т.И., Зарицкий А.Ю., Абдулкадыров К.М., Птушкин В.В., Цветаева Н.В., Лисуков И.А., Салогуб Г.Н., Голенков А.К., Медведева Н.В., Рукавицын О.А., Иванова В.Л., Маркова И.В. Рекомендации Российского Совета экспертов по диагностике и лечению больных первичной иммунной тромбоцитопенией. Онкогематология. 2010;(3):36-45.
For citation:
Maschan A.A., Rumyantsev A.G., Kovaleva L.G., Afanasiev B.V., Pospelova T.I., Zaritskiy A.Yu., Abdulkadyrov K.M., Ptushkin V.V., Tsvetaeva N.V., Lisukov I.A., Salogub G.N., Golenkov A.K., Medvedeva N.V., Rukavitsyn O.A., Ivanova V.L., Markova I.V. Guidelines of Russian Expert Council on diagnostic and therapy of patients with primary immunne thrombocytopenia. Oncohematology. 2010;(3):36-45. (In Russ.)