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Unspecified skin peripheral T-cell lymphoma: diagnostic difficulties

https://doi.org/10.17650/1818-8346-2020-15-3-63-66

Abstract

Peripheral T-cell lymphoma, not otherwise specified (PTCL-NOS) have an aggressive, life-threatening course. 5‑year survival rate is less than 20 %, which may be due to not timely diagnosis. PTCL-NOS can histologically and immunophenotypically mimic other T-cell lymphomas of the skin, including mycosis fungoides. In this connection, the correct diagnosis is most often established in the late stages of the disease. We present a clinical case of PTCL-NOS misdiagnosed as mycosis fungoides.

About the Authors

O. Yu. Olisova
Department Skin and Venereal Diseases named after V. A. Rakhmanov, Institute of Clinical Medicine, I. M. Sechenov First Moscow State Medical University, Ministry of Health of Russia (Sechenov University)
Russian Federation
4, Build. 1 Bol’shaya Pirogovskaya St., Moscow 119991, Russia


E. Yu. Vertieva
Department Skin and Venereal Diseases named after V. A. Rakhmanov, Institute of Clinical Medicine, I. M. Sechenov First Moscow State Medical University, Ministry of Health of Russia (Sechenov University)
Russian Federation
4, Build. 1 Bol’shaya Pirogovskaya St., Moscow 119991, Russia


D. R. Amshinskaya
Department Skin and Venereal Diseases named after V. A. Rakhmanov, Institute of Clinical Medicine, I. M. Sechenov First Moscow State Medical University, Ministry of Health of Russia (Sechenov University)
Russian Federation
4, Build. 1 Bol’shaya Pirogovskaya St., Moscow 119991, Russia


M. G. Lecaillon
Department Skin and Venereal Diseases named after V. A. Rakhmanov, Institute of Clinical Medicine, I. M. Sechenov First Moscow State Medical University, Ministry of Health of Russia (Sechenov University)
Russian Federation
4, Build. 1 Bol’shaya Pirogovskaya St., Moscow 119991, Russia


E. V. Grekova
Department Skin and Venereal Diseases named after V. A. Rakhmanov, Institute of Clinical Medicine, I. M. Sechenov First Moscow State Medical University, Ministry of Health of Russia (Sechenov University)
Russian Federation
4, Build. 1 Bol’shaya Pirogovskaya St., Moscow 119991, Russia


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Review

For citations:


Olisova O.Yu., Vertieva E.Yu., Amshinskaya D.R., Lecaillon M.G., Grekova E.V. Unspecified skin peripheral T-cell lymphoma: diagnostic difficulties. Oncohematology. 2020;15(3):63-66. (In Russ.) https://doi.org/10.17650/1818-8346-2020-15-3-63-66

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ISSN 1818-8346 (Print)
ISSN 2413-4023 (Online)