OncohematologyOncohematologyОнкогематология1818-83462413-4023Publishing House ABV Press3210.17650/1818-8346-2013-8-2-34-40HEMATOLOGIC MALIGNANCIES: DIAGNOSIS, TREATMENT, SUPPORTIVE CAREГЕМОБЛАСТОЗЫ: ДИАГНОСТИКА, ЛЕЧЕНИЕ, СОПРОВОДИТЕЛЬНАЯ ТЕРАПИЯSubcutaneous panniculitis-like T-cell lymphoma in children. Literature review and case reportsПодкожная панникулит-подобная Т-клеточная лимфома у детей. Обзор литературы и описание случаев из практикиAbramovD. S.АбрамовД. С.
Russian Federation

Pathology Department

Патологоанатомическое отделение

abramovd_s@bk.ruKonovalovD. M.КоноваловД. М.
Russian Federation

Pathology Department

Патологоанатомическое отделение

RogozhinD. V.РогожинД. В.
Russian Federation

Pathology Department

Pathology Department

 

Патологоанатомическое отделение

патологоанатомическое отделение

 

MyakovaN. V.МяковаН. В.
Russian Federation

Oncohematology Department

отделение онкогематологии

BiyachuevE. R.БиячуевЭ. Р.
Russian Federation

Adolescents and Young Adults Hematology/Oncology Department

отделение гематологии/онкологии для подростков и молодых взрослых

RoshchinV. Yu.РощинВ. Ю.
Russian Federation

Pathology Department

Патологоанатомическое отделение

MitrofanovaA. M.МитрофановаА. М.
Russian Federation

Pathology Department

Патологоанатомическое отделение

KislyakovA. N.КисляковА. Н.
Russian Federation

Pathology Department

Патологоанатомическое отделение

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of RussiaФГБУ «Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава РоссииFederal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of Russia Russian Children Clinical Hospital, Ministry of Health of RussiaФГБУ «Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России ФГБУ «Российская детская клиническая больница» Минздрава РоссииFederal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of RussiaФГБУ ФНКЦ ДГОИ им. Дмитрия Рогачева Минздрава РоссииFederal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of RussiaФГБУ ФНКЦ ДГОИ им. Дмитрия Рогачева Минздрава России2205201382344021072014210720142013https://oncohematology.abvpress.ru/ongm/article/view/32

Subcutaneous panniculitis-like T-cell lymphoma (SPTL) is a rare tumor from αβ mature cytotoxic T-lymphocytes, which primarily affects the subcutaneous adipose tissue and has morphological manifestations similar to panniculitis. SPTL frequency is less than 1 % of all NHL. It occurs in all age groups, but only 19–20 % are patients younger 20 years. Median age of patients is 35–36 years. To date are only a few cases in children described. In this article we described 3 SPTL cases in patients 1, 10 and 17 years old with typical clinical presentation and detailed analysis.

Подкожная панникулит-подобная Т-клеточная лимфома (ППТЛ) – редкая опухоль из зрелых цитотоксических αβ Т-лимфоцитов, которая первично поражает подкожную жировую ткань и имеет морфологические проявления, напоминающие панникулит. Частота ППТЛ составляет менее 1 % всех неходжкинских лимфом, встречается во всех возрастных группах, только 19–20 % составляют пациенты младше 20 лет, медиана возраста 35–36 лет. У детей описаны лишь единичные случаи. В данной статье представлены 3 случая ППТЛ у больных 1, 10 и 17 лет с типичным клиническим симптомокомплексом и подробным диагностическим анализом.

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