Case of congenital Langerhans cells histiocytosis in an infant

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Abstract

In this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characterized. Authors concluded that timely diagnostics is very important to risk-adapted therapy at children with LCH.

About the authors

T. T. Valiev

Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Author for correspondence.
Email: timurvaliev@mail.ru
Russian Federation

L. A. Makhonova

Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

A. M. Kovrigina

Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

E. N. Sholokhova

Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

N. N. Tupitsyn

Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

I. N. Serebryakova

Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

G. L. Mentkevich

Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences

Russian Federation

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