Case of congenital Langerhans cells histiocytosis in an infant
- Authors: Valiev T.T.1, Makhonova L.A.1, Kovrigina A.M.2, Sholokhova E.N.2, Tupitsyn N.N.2, Serebryakova I.N.1, Mentkevich G.L.1
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Affiliations:
- Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
- Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
- Issue: Vol 6, No 2 (2011)
- Pages: 19-22
- Section: HEMATOLOGIC MALIGNANCIES: DIAGNOSIS, TREATMENT, SUPPORTIVE CARE
- Published: 23.05.2011
- URL: https://oncohematology.abvpress.ru/ongm/article/view/98
- DOI: https://doi.org/10.17650/1818-8346-2011-6-2-19-22
- ID: 98
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Abstract
In this article a rare case of monosystem form of congenital Langerhans cells histiocytosis (LCH) in 3 weeks of age girl was described. Local lesion of oral mucosa of the infant with LCH was first described. Morphological, immunological and clinical features of this rare disease have been characterized. Authors concluded that timely diagnostics is very important to risk-adapted therapy at children with LCH.
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About the authors
T. T. Valiev
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical Sciences
Author for correspondence.
Email: timurvaliev@mail.ru
Russian Federation
L. A. Makhonova
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
A. M. Kovrigina
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
E. N. Sholokhova
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
N. N. Tupitsyn
Institute of Clinical Oncology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
I. N. Serebryakova
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
G. L. Mentkevich
Institute of Pediatric Oncology and Hematology, N.N. Blokhin Russian Cancer Research Center, Russian Academy of Medical SciencesRussian Federation
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