Immune thrombocytopenia: clinical manifestation and therapy response. The interim analysis of Russian register of patients with primary immune thrombocytopenia and literature review
- Authors: Lisukov I.A.1, Maschan A.A.2, Shamardina A.V.3, Chagorova T.V.4, Davydkin I.L.5, Sycheva T.M.6, Zagoskina T.P.7, Karyagina E.V.8, Salogub G.N.9, Savinova M.T.10, Shelekhova T.V.11, Kovaleva L.G.12, Shneyder T.V.13, Unzhekova A.N.14, Kuznetsova E.E.15, Shatokhin Y.V.16, Ivanova M.O.17, Vinogradova E.Y.18, Volodicheva E.M.15, Markova I.V.1, Kanyukova O.V.19, Abdulkadyrov K.M.20, Sedlova Y.A.15, Osyunikhina S.M.21, Kaplanov K.D.22, Tsvetaeva N.V.12, Akhmadeev A.R.23, Uspenskaya O.S.24, Kulagin A.D.24, Medvedeva N.V.25, Rumyantsev A.G.2, Afanasiev B.V.24
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Affiliations:
- Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia
- Dmitriy Rogachev Federal Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia
- Regional Children Clinical Hospital
- Regional Oncologic Dispensary
- Samara State Medical University, Ministry of Health of Russia
- Alexander-and-Mary Regional Clinical Hospital
- Kirov Research Centre of Hematology and Transfusiology, Federal Medical Biological Agency
- City Clinical Hospital № 15
- St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia
- City Clinical Hospital № 16
- Hematology Clinic, V.I. Razumovskiy Saratov State Medical University
- Hematological Research Centre, Ministry of Health of Russia
- Leningrad Regional Clinical Hospital
- Perm Territorial Clinical Hospital
- Regional Clinical Hospital
- Rostov State Medical University, Ministry of Health of Russia
- I.P. Pavlov State Medical University, Ministry of Health of Russia
- Territorial Clinical Hospital
- Clinical Medical Unit № 1
- Russian Research Institute of Hematology and Transfusiology, Russian Federal Medico-biological Agency
- City Clinical Hospital № 4
- Regional Oncologic Clinical Dispensary № 1
- Republic Clinical Hospital
- Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia
- City Hospital № 31
- Issue: Vol 8, No 2 (2013)
- Pages: 61-69
- Section: PHARMACOTHERAPY
- Published: 22.05.2013
- URL: https://oncohematology.abvpress.ru/ongm/article/view/35
- DOI: https://doi.org/10.17650/1818-8346-2013-8-2-61-69
- ID: 35
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Abstract
Primary immune thrombocytopenia (ITP) is a rare (orphan) blood disease. Most frequent manifestations of ITP are purpura, petechiae and bleedings with many patients have either no symptoms or minimal bleedings manifestation. The management of ITP varies widely and must be based on current international recommendations and individual assessment of clinical course. The paper presents the results of interim analysis of clinical course and therapeutic approaches in the Russian register of ITP patients with immune thrombocytopenia and literature review about ITP treatment approaches.
About the authors
I. A. Lisukov
Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University,Ministry of Health of Russia
Author for correspondence.
Email: igor_lisukov@mail.ru
Russian Federation
A. A. Maschan
Dmitriy Rogachev Federal Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of RussiaRussian Federation
A. V. Shamardina
Regional Children Clinical HospitalRussian Federation
T. V. Chagorova
Regional Oncologic DispensaryRussian Federation
I. L. Davydkin
Samara State Medical University, Ministry of Health of RussiaRussian Federation
T. M. Sycheva
Alexander-and-Mary Regional Clinical HospitalRussian Federation
T. P. Zagoskina
Kirov Research Centre of Hematology and Transfusiology, Federal Medical Biological AgencyRussian Federation
E. V. Karyagina
City Clinical Hospital № 15Russian Federation
G. N. Salogub
St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russiaкафедра факультетской терапии Russian Federation
M. T. Savinova
City Clinical Hospital № 16Russian Federation
T. V. Shelekhova
Hematology Clinic, V.I. Razumovskiy Saratov State Medical Universityклиника гематологии Russian Federation
L. G. Kovaleva
Hematological Research Centre, Ministry of Health of RussiaRussian Federation
T. V. Shneyder
Leningrad Regional Clinical HospitalRussian Federation
A. N. Unzhekova
Perm Territorial Clinical HospitalRussian Federation
E. E. Kuznetsova
Regional Clinical HospitalRussian Federation
Yu. V. Shatokhin
Rostov State Medical University, Ministry of Health of RussiaRussian Federation
M. O. Ivanova
I.P. Pavlov State Medical University, Ministry of Health of RussiaClinical Diagnostic Center “Clinics” Russian Federation
E. Yu. Vinogradova
Territorial Clinical HospitalRussian Federation
E. M. Volodicheva
Regional Clinical HospitalRussian Federation
I. V. Markova
Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University,Ministry of Health of Russia
Russian Federation
O. V. Kanyukova
Clinical Medical Unit № 1Russian Federation
K. M. Abdulkadyrov
Russian Research Institute of Hematology and Transfusiology, Russian Federal Medico-biological AgencyRussian Federation
Yu. A. Sedlova
Regional Clinical HospitalRussian Federation
S. M. Osyunikhina
City Clinical Hospital № 4Russian Federation
K. D. Kaplanov
Regional Oncologic Clinical Dispensary № 1Russian Federation
N. V. Tsvetaeva
Hematological Research Centre, Ministry of Health of RussiaRussian Federation
A. R. Akhmadeev
Republic Clinical HospitalRussian Federation
O. S. Uspenskaya
Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of RussiaRussian Federation
A. D. Kulagin
Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of RussiaRussian Federation
N. V. Medvedeva
City Hospital № 31Russian Federation
A. G. Rumyantsev
Dmitriy Rogachev Federal Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of RussiaRussian Federation
B. V. Afanasiev
Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of RussiaRussian Federation
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