Immune thrombocytopenia: clinical manifestation and therapy response. The interim analysis of Russian register of patients with primary immune thrombocytopenia and literature review

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Abstract

Primary immune thrombocytopenia (ITP) is a rare (orphan) blood disease. Most frequent manifestations of ITP are purpura, petechiae and bleedings with many patients have either no symptoms or minimal bleedings manifestation. The management of ITP varies widely and must be based on current international recommendations and individual assessment of clinical course. The paper presents the results of interim analysis of clinical course and therapeutic approaches in the Russian register of ITP patients with immune thrombocytopenia and literature review about ITP treatment approaches.

About the authors

I. A. Lisukov

Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University,
Ministry of Health of Russia

Author for correspondence.
Email: igor_lisukov@mail.ru
Russian Federation

A. A. Maschan

Dmitriy Rogachev Federal Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia

Russian Federation

A. V. Shamardina

Regional Children Clinical Hospital

Russian Federation

T. V. Chagorova

Regional Oncologic Dispensary

Russian Federation

I. L. Davydkin

Samara State Medical University, Ministry of Health of Russia

Russian Federation

T. M. Sycheva

Alexander-and-Mary Regional Clinical Hospital

Russian Federation

T. P. Zagoskina

Kirov Research Centre of Hematology and Transfusiology, Federal Medical Biological Agency

Russian Federation

E. V. Karyagina

City Clinical Hospital № 15

Russian Federation

G. N. Salogub

St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia

кафедра факультетской терапии Russian Federation

M. T. Savinova

City Clinical Hospital № 16

Russian Federation

T. V. Shelekhova

Hematology Clinic, V.I. Razumovskiy Saratov State Medical University

клиника гематологии Russian Federation

L. G. Kovaleva

Hematological Research Centre, Ministry of Health of Russia

Russian Federation

T. V. Shneyder

Leningrad Regional Clinical Hospital

Russian Federation

A. N. Unzhekova

Perm Territorial Clinical Hospital

Russian Federation

E. E. Kuznetsova

Regional Clinical Hospital

Russian Federation

Yu. V. Shatokhin

Rostov State Medical University, Ministry of Health of Russia

Russian Federation

M. O. Ivanova

I.P. Pavlov State Medical University, Ministry of Health of Russia

Clinical Diagnostic Center “Clinics” Russian Federation

E. Yu. Vinogradova

Territorial Clinical Hospital

Russian Federation

E. M. Volodicheva

Regional Clinical Hospital

Russian Federation

I. V. Markova

Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University,
Ministry of Health of Russia

Russian Federation

O. V. Kanyukova

Clinical Medical Unit № 1

Russian Federation

K. M. Abdulkadyrov

Russian Research Institute of Hematology and Transfusiology, Russian Federal Medico-biological Agency

Russian Federation

Yu. A. Sedlova

Regional Clinical Hospital

Russian Federation

S. M. Osyunikhina

City Clinical Hospital № 4

Russian Federation

K. D. Kaplanov

Regional Oncologic Clinical Dispensary № 1

Russian Federation

N. V. Tsvetaeva

Hematological Research Centre, Ministry of Health of Russia

Russian Federation

A. R. Akhmadeev

Republic Clinical Hospital

Russian Federation

O. S. Uspenskaya

Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia

Russian Federation

A. D. Kulagin

Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia

Russian Federation

N. V. Medvedeva

City Hospital № 31

Russian Federation

A. G. Rumyantsev

Dmitriy Rogachev Federal Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia

Russian Federation

B. V. Afanasiev

Raisa Gorbacheva Memorial Institute of Children Hematology and Transplantation, St.-Petersburg I.P. Pavlov State Medical University, Ministry of Health of Russia

Russian Federation

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