Subcutaneous panniculitis-like T-cell lymphoma in children. Literature review and case reports

Cover Page

Cite item

Full Text

Abstract

Subcutaneous panniculitis-like T-cell lymphoma (SPTL) is a rare tumor from αβ mature cytotoxic T-lymphocytes, which primarily affects the subcutaneous adipose tissue and has morphological manifestations similar to panniculitis. SPTL frequency is less than 1 % of all NHL. It occurs in all age groups, but only 19–20 % are patients younger 20 years. Median age of patients is 35–36 years. To date are only a few cases in children described. In this article we described 3 SPTL cases in patients 1, 10 and 17 years old with typical clinical presentation and detailed analysis.

About the authors

D. S. Abramov

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Author for correspondence.
Email: abramovd_s@bk.ru
Pathology Department Russian Federation

D. M. Konovalov

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Pathology Department Russian Federation

D. V. Rogozhin

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Russian Children Clinical Hospital, Ministry of Health of Russia

Pathology Department

Pathology Department

 

Russian Federation

N. V. Myakova

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Oncohematology Department Russian Federation

E. R. Biyachuev

Federal Research Center of Hematology,
Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of Russia

Adolescents and Young Adults Hematology/Oncology Department Russian Federation

V. Yu. Roshchin

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Pathology Department Russian Federation

A. M. Mitrofanova

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Pathology Department Russian Federation

A. N. Kislyakov

Federal Research Center of Hematology, Oncology and Immunology named after Dmitriy Rogachev,
Ministry of Health of Russia

Pathology Department Russian Federation

References

Supplementary files

Supplementary Files
Action
1. JATS XML

Copyright (c) 2013



СМИ зарегистрировано Федеральной службой по надзору в сфере связи, информационных технологий и массовых коммуникаций (Роскомнадзор).
Регистрационный номер и дата принятия решения о регистрации СМИ: серия ПИ № ФС 77-36928 от  21.07.2009.