Extranodal NK/T-cell lymphoma: a review of literature and case report

Abstract

Extranodal NK/T-cell lymphoma – a rare lymphoproliferative disease characterized predominantly by extranodal localization, aggressive course and low efficiency of conventional chemotherapy. Clinical presentation is diverse and depends on tumor lesion localization. In this article, a literature review and case report of patient with generalized extranodal NK/T-cell lymphoma with bone marrow involvement, unusual intracranial tumor localization, tumor leukemization and central nervous system-leukemia were presented. Adequate treatment strategy made it possible to achieve long-term complete remission in a patient with poor prognosis.

About the authors

N. G. Chernova

Research Center for Hematology, Ministry of Health of Russia

Author for correspondence.
Email: ngchernova@mail.ru
Russian Federation

M. V. Nareyko

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

M. N. Sinitsyna

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

Yu. V. Sidorova

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

G. A. Yatsy

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

A. M. Kovrigina

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

E. E. Zvonkov

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

V. N. Dvirnyk

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

L. A. Kuz’mina

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

E. N. Parovichnikova

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

V. G. Savchenko

Research Center for Hematology, Ministry of Health of Russia

Russian Federation

References

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